Matthew McKenzie

Comparison of log P values obtained from CAChe and other sources.

Functional respiratory chain analyses in murid xenomitochondrial cybrids expose coevolutionary constraints of cytochrome b and nuclear subunits of complex III.

Production of homoplasmic xenomitochondrial mice.

Mitochondrial disease: mutations and mechanisms.

Unravelling the peculiar nucleation mechanisms for non-ideal binary mixtures with atomistic simulations.

Mitochondrial respiratory chain supercomplexes are destabilized in Barth Syndrome patients.

Probing the nucleation mechanism for the binary n-nonane/1-alcohol series with atomistic simulations.

Analysis of mitochondrial subunit assembly into respiratory chain complexes using Blue Native polyacrylamide gel electrophoresis.

Analysis of the assembly profiles for mitochondrial- and nuclear-DNA-encoded subunits into complex I.

Mitochondrial ND5 gene variation associated with encephalomyopathy and mitochondrial ATP consumption.

Assembly of mitochondrial complex I and defects in disease.

Mutation of C20orf7 disrupts complex I assembly and causes lethal neonatal mitochondrial disease.

Chapter 18 Analysis of respiratory chain complex assembly with radiolabeled nuclear- and mitochondrial-encoded subunits.

Assembly of nuclear DNA-encoded subunits into mitochondrial complex IV, and their preferential integration into supercomplex forms in patient mitochondria.

Mitochondrial cardiolipin involved in outer-membrane protein biogenesis: implications for Barth syndrome.

Assembly factors of human mitochondrial complex I and their defects in disease.

Mutation of the mitochondrial tyrosyl-tRNA synthetase gene, YARS2, causes myopathy, lactic acidosis, and sideroblastic anemia--MLASA syndrome.

Mutations in MTFMT underlie a human disorder of formylation causing impaired mitochondrial translation.

Understanding mitochondrial complex I assembly in health and disease.

The effects of nuclear reprogramming on mitochondrial DNA replication.

Mutations in the gene encoding C8orf38 block complex I assembly by inhibiting production of the mitochondria-encoded subunit ND1.

Next-generation sequencing in molecular diagnosis: NUBPL mutations highlight the challenges of variant detection and interpretation.

Timely attention to staffing.

Proteomic and metabolomic analyses of mitochondrial complex I-deficient mouse model generated by spontaneous B2 short interspersed nuclear element (SINE) insertion into NADH dehydrogenase (ubiquinone) Fe-S protein 4 (Ndufs4) gene.

Mitochondrial DNA copy number is regulated in a tissue specific manner by DNA methylation of the nuclear-encoded DNA polymerase gamma A.

Mitochondrial dysfunction in a novel form of autosomal recessive ataxia.

Mitochondrial DNA haplotypes define gene expression patterns in pluripotent and differentiating embryonic stem cells.

Modulation of ceramide-induced cell death and superoxide production by mitochondrial DNA-encoded respiratory chain defects in Rattus xenocybrid mouse cells.

Clostridium difficile infection: a multicenter study of epidemiology and outcomes in mechanically ventilated patients.

Fluid balance and cardiac function in septic shock as predictors of hospital mortality.

The identification of mitochondrial DNA variants in glioblastoma multiforme.

A founder mutation in PET100 causes isolated complex IV deficiency in Lebanese individuals with Leigh syndrome.

Mitochondrial research in Australia: a major player in worldwide trends.

Effects of empiric antifungal therapy for septic shock on time to appropriate therapy for Candida infection: a pilot study.

Critical review of bronchial thermoplasty: where should it fit into asthma therapy?

Capture of somatic mtDNA point mutations with severe effects on oxidative phosphorylation in synaptosome cybrid clones from human brain.

Characterization of mitochondrial FOXRED1 in the assembly of respiratory chain complex I.

Anti-cancer analogues ME-143 and ME-344 exert toxicity by directly inhibiting mitochondrial NADH: ubiquinone oxidoreductase (Complex I).

Conservation implications of omitting historical data sources: response to Baisre.

Generation of Xenomitochondrial Embryonic Stem Cells for the Production of Live Xenomitochondrial Mice.

Dietary interventions designed to protect the perinatal brain from hypoxic-ischemic encephalopathy--Creatine prophylaxis and the need for multi-organ protection.

Hydrogel-Based Drug Delivery Systems for Poorly Water-Soluble Drugs.

Deletion of the Complex I Subunit NDUFS4 Adversely Modulates Cellular Differentiation.

Analysis of Mitochondrial DNA in Induced Pluripotent and Embryonic Stem Cells.

Combined defects in oxidative phosphorylation and fatty acid β-oxidation in mitochondrial disease.

AarF Domain Containing Kinase 3 (ADCK3) Mutant Cells Display Signs of Oxidative Stress, Defects in Mitochondrial Homeostasis and Lysosomal Accumulation.

Loss of mitochondrial DNA-encoded protein ND1 results in disruption of complex I biogenesis during early stages of assembly.

Vitamin D3 therapy in patients with asthma complicated by sinonasal disease: Secondary analysis of the Vitamin D Add-on Therapy Enhances Corticosteroid Responsiveness in Asthma trial.

Restoration of normal embryogenesis by mitochondrial supplementation in pig oocytes exhibiting mitochondrial DNA deficiency.

Impaired Cellular Bioenergetics Causes Mitochondrial Calcium Handling Defects in MT-ND5 Mutant Cybrids.

Proof-of-Concept of Polymeric Sol-Gels in Multi-Drug Delivery and Intraoperative Image-Guided Surgery for Peritoneal Ovarian Cancer.

Correction: AarF Domain Containing Kinase 3 (ADCK3) Mutant Cells Display Signs of Oxidative Stress, Defects in Mitochondrial Homeostasis and Lysosomal Accumulation.

Tim29 is a novel subunit of the human TIM22 translocase and is involved in complex assembly and stability.

Monocytes and dendritic cells are the primary sources of interleukin 37 in human immune cells.