Ernesto R. Bongarzone

Central nervous system myelination in mice with deficient expression of Notch1 receptor.

Myelin: development, disorders and neural repair. A satellite meeting of the International and American Societies for Neurochemistry joint meeting in Buenos Aires. Bastion del Carmen, September 1-4, 2001, Colonia, Uruguay.

Induction of oligodendrocyte fate during the formation of the vertebrate neural tube.

Notch1 and Numb genes are inversely expressed as oligodendrocytes differentiate.

Soma-restricted products of the myelin proteolipid gene are expressed primarily in neurons in the developing mouse nervous system.

Expression of soma-restricted proteolipid/DM20 proteins in lymphoid cells.

Identification of a protein that interacts with the golli-myelin basic protein and with nuclear LIM interactor in the nervous system.

Embryonic expression of the soma-restricted products of the myelin proteolipid gene in motor neurons and muscle.

Axons mediate the distribution of arylsulfatase A within the mouse hippocampus upon gene delivery.

Notch signaling in astrocytes and neuroblasts of the adult subventricular zone in health and after cortical injury.

Neural stem/progenitor cells participate in the regenerative response to perinatal hypoxia/ischemia.

Effects of irradiation on the postnatal development of the brain in a genetic mouse model of globoid cell leukodystrophy.

Autonomic denervation of lymphoid organs leads to epigenetic immune atrophy in a mouse model of Krabbe disease.

P2x7 deficiency suppresses development of experimental autoimmune encephalomyelitis.

Psychosine accumulates in membrane microdomains in the brain of krabbe patients, disrupting the raft architecture.

Peripheral neuropathy in the Twitcher mouse involves the activation of axonal caspase 3.

Psychosine induces the dephosphorylation of neurofilaments by deregulation of PP1 and PP2A phosphatases.

Detection of the neurotoxin psychosine in samples of peripheral blood: application in diagnostics and follow-up of Krabbe disease.

MMP-3 mediates psychosine-induced globoid cell formation: implications for leukodystrophy pathology.

Missense mutation in mouse GALC mimics human gene defect and offers new insights into Krabbe disease.

The sphingolipid psychosine inhibits fast axonal transport in Krabbe disease by activation of GSK3β and deregulation of molecular motors.

Inhibition of angiogenesis by β-galactosylceramidase deficiency in globoid cell leukodystrophy.

Characterization and application of a disease-cell model for a neurodegenerative lysosomal disease.

Neuronal inclusions of α-synuclein contribute to the pathogenesis of Krabbe disease.

Vitamin C Transporters, Recycling and the Bystander Effect in the Nervous System: SVCT2 versus Gluts.

Aberrant production of tenascin-C in globoid cell leukodystrophy alters psychosine-induced microglial functions.